Ведение пациентов с аутоиммунным панкреатитом


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Введение

Аутоиммунный панкреатит (АИП) - это редкая, но хорошо изученная форма воспаления поджелудочной железы. В отличие от других заболеваний поджелудочной железы, оно обычно демонстрирует выраженный ответ на терапию глюкокортикоидами. Рентгенологически AИП может проявляться как очаговое образование, неотличимое от рака поджелудочной железы, или как диффузный процесс в поджелудочной железе, который может быть патогномоничным для AИП. При отсутствии лечения, АИП может привести к панкреатической недостаточности, фиброзу и другим осложнениям. Первоначальное обнаружение повышенного уровня иммуноглобулина G4 (IgG4) в качестве биомаркера АИП помогло установить, что это заболевание отличается от других форм хронического панкреатита. Однако сейчас известно, что уровень IgG4 при АИП часто бывает нормальным и что при других заболеваниях, таких как рак поджелудочной железы, уровень IgG4 может быть умеренно повышен.

Индукция ремиссии
Последующее ведение
Мониторинг долгосрочных осложнений
Резюме
Источники литературы