L-транспозиция магистральных артерий: лечение и исходы


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Введение

Левосторонняя или L-петлевая транспозиция магистральных артерий (L-TMA) - редкая форма врожденного порока сердца, характеризующаяся атриовентрикулярной (АВ) и вентрикуло-артериальной дискордантностью. Ее также принято называть врожденной корригированной ТМА, двойной дискордантностью или инверсией желудочков.

L-TMA обычно не сопровождается цианозом, если нет сопутствующих пороков сердца. Изолированная L-TMA «физиологически скорректирована», поскольку системная дезоксигенированная венозная кровь возвращается в легочную циркуляцию, а оксигенированная легочная венозная кровь возвращается в системную циркуляцию. Пациенты с L-TMA имеют повышенный риск развития сердечной недостаточности во взрослом возрасте из-за прогрессирующего снижения системной функции правого желудочка (ПЖ).

Здесь будут представлены методы лечения и исходы L-TMA.

Хирургическое лечение
Исходы
Последующее наблюдение
Беременность
Анатомия нормального сердца и врожденно корригированной транспозиции магистральных артерий (L-ТМА)
Резюме
Список литературы
Разделы:
Кардиология