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Введение
Амилоидоз представляет собой внеклеточное отложение фибрилл, возникающих из ряда сывороточных белков. Эти фибриллы имеют бета-складчатую конфигурацию, что приводит к характерным гистологическим изменениям [1]. Амилоидные отложения могут возникать в различных органах, но наиболее значимые клинические последствия, включая смертность, развиваются при поражении сердца, почек, печени или вегетативной нервной системы.
В данном разделе рассматриваются лечение и прогноз при амилоидозе сердца.
Специфические осложнения амилоидоза
AL-амилоидоз сердца
ATTR-амилоидоз
АА-амилоидоз и другие виды амилоидоза
Резюме
Список литературы
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